A Case of IgG4 Associated Sclerosing Cholangitis without Clinical Manifestations of Autoimmune Pancreatitis.
- Author:
Song Wook CHUN
1
;
Ja Sung CHOI
;
Beo Deul KANG
;
Yu Jin KIM
;
Ki Jun HAN
;
Hyeon Geun CHO
;
Hwa Eun OH
;
Jae Hee CHO
Author Information
- Publication Type:Case Reports ; English Abstract
- Keywords: Immunoglobulin G4; Cholangitis, sclerosing; Pancreatitis; Cholangiocarcinoma
- MeSH: Aged; Anti-Inflammatory Agents/therapeutic use; Autoimmune Diseases/complications/diagnosis; Bile Ducts, Intrahepatic/pathology/ultrasonography; Cholangiopancreatography, Endoscopic Retrograde; Cholangitis, Sclerosing/complications/*diagnosis/drug therapy; Common Bile Duct/pathology/ultrasonography; Humans; Immunoglobulin G/*blood; Immunohistochemistry; Male; Pancreatitis/complications/diagnosis; Prednisolone/therapeutic use; Tomography, X-Ray Computed
- From:The Korean Journal of Gastroenterology 2013;62(1):69-74
- CountryRepublic of Korea
- Language:Korean
- Abstract: IgG4-related systemic diseases are characterized by a diffuse or mass forming inflammatory reaction rich in lymphocytes and IgG4-positive plasma cells (lymphoplasmacytic infiltration), fibrosclerosis of variable organs and obliterative phlebitis. They usually involve various organs including the pancreas, bile duct, gallbladder, salivary gland, retroperitoneum, kidney, lung, and prostate. However, most of them are accompanied by autoimmune pancreatitis, and good response to steroid treatment is one of the hallmarks of this disease. We report a case of an 67-year-old man with IgG4 associated sclerosing cholangitis, who was diagnosed by endoscopic retrograde cholangiopancreatography and successfully treated with steroid therapy.
