Isolated Left Ventricular Noncompaction Cardiomyopathy Accompanied by Severe Mitral Regurgitation.
10.4070/kcj.2009.39.11.494
- Author:
Jong Won CHUNG
1
;
Sung Jin LEE
;
Jae Hak LEE
;
Jung Yeon CHIN
;
Hyo Jin LEE
;
Chang Jung LEE
;
Yun Seok CHOI
;
Sung Bo SHIM
;
Ho Joong YOUN
;
Sun Hee LEE
Author Information
1. Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea, St. Mary's Hospital, Seoul, Korea. younhj@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Cardiomyopathies;
Mitral valve regurgitation
- MeSH:
Cardiomyopathies;
Dyspnea;
Echocardiography, Doppler;
Embryonic Development;
Emergencies;
Endocardium;
Female;
Heart Atria;
Heart Ventricles;
Humans;
Korea;
Mitral Valve;
Mitral Valve Insufficiency;
Myocardium;
Pregnancy;
Prolapse;
Rupture;
Young Adult
- From:Korean Circulation Journal
2009;39(11):494-498
- CountryRepublic of Korea
- Language:English
-
Abstract:
Isolated left ventricular noncompaction cardiomyopathy (IVNC) is a cardiomyopathy thought to be caused by arrest of normal embryogenesis of the endocardium and myocardium. This abnormality is often associated with other congenital cardiac defects. A 21-year-old man presented to the emergency department with worsening exertional dyspnea during the previous 2 months. Two-dimensional and Doppler echocardiography revealed an enlarged left atrium (LA) and a markedly dilated left ventricle (LV) with preserved LV systolic function, severe mitral valve regurgitation, and prolapse due to chordae rupture. The myocardium of the LV and right ventricle (RV) had excessively prominent trabeculations and deep intertrabecular recesses. He is the first patient in Korea who has undergone mitral valve replacement surgery because of severe mitral valve regurgitation and prolapse due to chordae rupture accompanied by IVNC.
