Melanotic Neuroectodermal Tumor of Infancy in the Epididymis: A Case Report.
- Author:
Sang Bae LEE
1
;
Seong Hun LEE
;
Min Hyuk RYU
;
Ji Seoung PARK
;
Joo Heoun YANG
;
Sun Young KIM
;
Dong Jean LEE
Author Information
1. Department of Pediatrics, Dong Kang General Hospital, Ulsan, Korea. djleekr@hanmail.net
- Publication Type:Case Report
- Keywords:
Melanotic neuroectodermal tumor of infancy;
Epididymis
- MeSH:
Epididymis*;
Head;
Humans;
Infant;
Male;
Maxilla;
Neck;
Neural Crest;
Neuroectodermal Tumor, Melanotic*;
Orchiectomy
- From:Korean Journal of Pediatrics
2004;47(12):1334-1337
- CountryRepublic of Korea
- Language:English
-
Abstract:
Melanotic neuroectodermal tumor of infancy (MNTI) is a rare neoplasm known by a variety of names including melanotic progonoma and retinal anlage tumor, and currently thought to be neural crest derivation. The vast majority develop within the first year of life. The behavior is generally benign, but recurrent and metastatic cases have been documented. It arises in the head and neck in over 90%, mainly in the maxilla, but is extremely rare in the epididymis. We report a case of MNTI together with a review of literature, which occurred in the right epididymis of a 6-month-old boy who presented with a painless, slowly growing, scrotal mass and was treated with radical orchiectomy.
