Clinical features of noncompaction of ventricular myocardium in children

VernacularTitle:儿童心肌致密化不全5例临床分析
Author: Qian NI ; Xiaoshuai WANG ; Yahong LIU ; Jin WANG ; Xiangyu DONG
Publication Type:Journal Article
Keywords: noncompaction of ventricular myocardium; clinical features; child
From: Journal of Clinical Pediatrics 2015;(3):254-257
CountryChina
Language:Chinese
Abstract: ObjectiveTo assess the clinical features of noncompaction of ventricular myocardium (NVM) in children. Methods The clinical data from ifve children with NVM were analyzed, including clinical manifestations, ultrasonic cardio-gram(UCG), electrocardiogram, chest X-ray, the process of diagnosis and treatment, and follow up.Results In ifve patients (3 boys and 2 girls) aged 3 months to 12 years, four of them were hospitalized because of pneumonia with heart failure. None of the ifve patients had thromboembolism. Heart enlargement was observed in all ifve patients on chest X-ray. By 2D ultrasonography, 2 patients had cardiac apex involvement, and 3 patients showed involvement of left ventricular wall and interventricular septum. In one patient, congenital partial defect of the endocardial cushion was observed. All patients were followed up for 3 to 36 months. One patient died of heart failure, 3 patients survived, and one patient was lost to follow-up.Conclusions The common clinical manifestation of NVM is the heart failure. UCG is preferred for NVM diagnosis. In children with refractory pneumonia and heart failure, NVM should be suspected.