Rosai-Dorfman Disease: Report of a Case Associated with IgG4-Related Sclerotic Lesions.
- Author:
Bong Hee PARK
1
;
Da Hye SON
;
Myung Hwan KIM
;
Tae Sun SHIM
;
Hee Jin LEE
;
Jooryung HUH
Author Information
1. Department of Pathology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea. jrhuh@amc.seoul.kr
- Publication Type:Case Report
- Keywords:
Rosai-Dorfman disease;
Histiocytosis, sinus;
Immunoglobulin G4
- MeSH:
Forearm;
Histiocytosis, Sinus;
Humans;
Lung;
Lymph Nodes;
Lymphatic Diseases;
Pancreatitis
- From:Korean Journal of Pathology
2012;46(6):583-586
- CountryRepublic of Korea
- Language:English
-
Abstract:
We describe a rare case of sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease) associated with a six-year history of autoimmune pancreatitis, which was controlled by steroid treatment. The patient presented with multiple, cervical and thoracic lymphadenopathy and abnormal, nodular opacities in the lung. Histologically, Rosai-Dorfman disease with numerous IgG4-positive cells was identified in a subcutaneous lymph node in the patient's left forearm. The patient recovered uneventfully with steroid treatment.
