A Case of Peritoneal Desmoplastic Small Round Cell Tumor which involved both ovaries.
- Author:
Jun Kyung KIM
1
;
Yun Sik LEE
;
Sun Nie AHN
;
Hong Cheun SHIN
;
Chun June LEE
;
Won Gyu KIM
;
Weon KIM
Author Information
1. Department of Obstetrics and Gynecology, Gospel Hospital, Kosin University, Busan, Korea. kwg@ns.kosinmed.or.kr
- Publication Type:Case Report
- Keywords:
Desmoplastic small round cell tumor;
Both ovaries
- MeSH:
Abdomen;
Child;
Desmoplastic Small Round Cell Tumor*;
Drug Therapy;
Female;
Humans;
Male;
Ovary*;
Pelvis;
Recurrence
- From:Korean Journal of Obstetrics and Gynecology
2006;49(1):224-229
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Peritoneal desmoplastic small round cell tumor is a very rare malignant neoplasm and has specific clinical features; It is predominant in children and young males and has a well-demarcated large intra-abdominal tumor, which has not been associated with a primary visceral organ, with diffusely scattered multiple small tumors and rarely involves ovaries. It is a very aggressive and fast growing tumor along the peritoneal surfaces of the abdomen and pelvis. It has a typical histologic features and a specific immunohistochemical staining pattern. There is no definite treatment. It responses to surgery and chemotherapy at early period of therapy but relapses soon and rapidly progresses and then causes the death. We have experienced a peritoneal desmoplastic small round cell tumor which involved both ovaries, so we report this case with a brief review of literature.
