Development and treatments of Kasabach-Merritt phenomenon
10.3760/cma.j.issn.2095-428X.2014.10.018
- VernacularTitle:Kasabach-Merritt现象的研究进展和治疗
- Author:
Yubin GONG
;
Bin SUN
;
Hongzhao LEI
;
Changxian DONG
- Publication Type:Journal Article
- Keywords:
Kasabach-Merritt phenomenon;
Hemangioma;
Thrombocytopenia;
Consumptive coagulopathy;
Kaposiform hemangioendothelioma;
Tufted angioma
- From:
Chinese Journal of Applied Clinical Pediatrics
2014;29(10):789-791
- CountryChina
- Language:Chinese
-
Abstract:
Kasabach-Merritt phenomenon (KMP) is characterized by thrombocytopenia with enlarging vascular tumour,KMP usually develops in infancy and is associated with significant morbidity and mortality,the mortality rate is reported as high as 30％.It commonly reported sites of tumor include extremities,trunk,retroperitoneum and neck.There is no consensus in treatment and various regimens have been used by different authors.This report is aim to learn the pathophysiology of the KMP and its diagnosis and treatment.
