Pheochromocytoma associated with cyanotic congenital heart disease.
- Author:
Seung Joon CHUNG
1
;
Young Ah LEE
;
Choong Ho SHIN
;
Sei Won YANG
;
Eun Jung BAE
;
Jung Il NOH
Author Information
- Publication Type:Case Report
- Keywords: Pheochromocytoma; Cyanotic; Hypoxia; Congenital heart defect; Diabetes mellitus
- MeSH: Anoxia; Diabetes Mellitus; Heart; Heart Defects, Congenital; Heart Diseases; Humans; Hypertension; Pheochromocytoma; Thoracic Surgery
- From:Korean Journal of Pediatrics 2008;51(1):93-97
- CountryRepublic of Korea
- Language:English
- Abstract: Pheochromocytoma is a rare tumor of childhood, arising from adrenal medullary and chromaffin tissue. Because chronic hypoxia may induce pheochromocytoma, there have been several reports of pheochromocytoma development in cyanotic patients after corrective or palliative cardiac surgery. The variable clinical presentation of pheochromocytoma is obscured by both underlying heart disease and medications. If sudden hypertension, aggravation of a heart condition, or unusual symptoms such as diabetes mellitus develops in a cyanotic patient with congenital heart disease, pheochromocytoma must be ruled out. We report two patients presenting with cyanotic single-ventricle heart disease with pheochromocytoma.
