Primary leiomyosarcoma of the chest wall in a child: a case report.
- Author:
Jae Hyuk CHOI
1
;
David Chanwook CHUNG
;
Mee Jeong LEE
Author Information
- Publication Type:Case Report
- Keywords: Leiomyosarcoma; Chest wall; Rib; Osteochondroma; Child
- MeSH: Child; Humans; Leiomyosarcoma; Muscle, Smooth; Osteochondroma; Ribs; Sarcoma; Thoracic Wall; Thorax
- From:Korean Journal of Pediatrics 2008;51(1):98-101
- CountryRepublic of Korea
- Language:English
- Abstract: Leiomyosarcoma is an uncommon soft tissue sarcoma of mesenchymal cell origin, which shows smooth muscle differentiation. Leiomyosarcoma is seldom found in the pediatric population, and accounts for fewer than 2% of all soft tissue sarcomas. Leiomyosarcoma of the chest wall is extremely rare in children. We report here a case of an 8-year-old boy with a primary leiomyosarcoma that was incidentally found as a rib mass. The patient underwent a complete resection for a suspected osteochondroma diagnosed by a three-dimensional chest computed tomography examination. Pathological findings of the mass revealed intersecting fascicles of spindle cells showing cigar-shaped nuclei, inconspicuous nuclear pleomorphism and occasional mitotic figures in the background of a suspected osteochondroma of the rib. This report documents the first description of a leiomyosarcoma possibly arising in an osteochondroma of the rib in a child.
