Two Cases of Topless Optic Disc Syndrome.
- Author:
Tae Woo KIM
1
;
Ki Chul SHIN
;
Dong Myung KIM
Author Information
1. Department of Ophthalmology, Seoul National University College of Medicine, 28 Yeongon-dong, Chongro-ku, Seoul, 110-744, Korea.
- Publication Type:Case Report
- Keywords:
Topless optic disc syndrome;
Optic nerve hypoplasia;
Glaucomatous optic nerve damage
- MeSH:
Atrophy;
Female;
Humans;
Nerve Fibers;
Optic Nerve;
Retinal Vessels;
Retinaldehyde;
Risk Factors;
Visual Acuity;
Visual Fields
- From:Journal of the Korean Ophthalmological Society
2000;41(10):2291-2295
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Topless optic disc syndrome is considered as congenital optic nerve hypoplasia.The risk factors of this syndrome are female sex, prematurity and history of maternal diabetes.Normal central visual acuity, thinning of superior peripapillary nerve fiber layer and corresponding inferior visual field defects are the characteristic features of this syndrome.Relative superior entrance of central retinal vessels and superior scleral halo can be found in patients with this syndrome. We experienced two cases of topless optic disc syndrome :one was unilateral and the other, bilateral. They had no history of maternal diabetes. Diffuse superior retinal nerve fiber layer atrophy and inferior visual field defects were observed.Pallor of superior optic neural rim, relative superior entrance of central retinal vessels and superior scleral halo were also observed. It will be necessary to differentiate these findings from glaucomatous optic disc damage and visual field defects.
