Anesthetic experience of a patient with hereditary factor XI deficiency (Hemophilia C) : A case report.
10.4097/kjae.2009.56.6.706
- Author:
Yee Suk KIM
1
;
Eun Yong CHUNG
;
Jun Rho YOON
;
In Soo HAN
;
Ah Reum PARK
;
Tae Kwan KIM
;
Chul Woo LEE
Author Information
1. Department of Anesthesiology and Pain Medicine, College of Medicine, The Catholic University of Korea, Seoul, Korea. 3tkkim@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
aPTT;
Factor XI deficiency;
Frontoethmoidectomy
- MeSH:
Epistaxis;
Factor XI;
Factor XI Deficiency;
Hemophilia A;
Humans;
Jews;
Plasma
- From:Korean Journal of Anesthesiology
2009;56(6):706-708
- CountryRepublic of Korea
- Language:English
-
Abstract:
Factor XI deficiency (also called Hemophilia C) rarely occurs among ethnicities other than Ashkenazi Jews. A boy was scheduled for frontoethmoidectomy due to bilateral chronic rhinosinusitis. He was incidentally found to have factor XI deficiency due to prolonged aPTT on preoperative laboratory finding. His medical history reveals frequent epistaxis 2 or 3 times per day and his factor XI and XII activity were 17% (normal; 60-140%) and 34% (normal; 60-140%), respectively on furthermore laboratory evaluation. He was diagnosed as hereditary factor XI deficiency. He underwent the operation with administration of the fresh frozen plasma without complication.
