Surgical treatment of hemangioma of limbs associated with Kasabach-Merritt phenomenon

VernacularTitle:肢体血管瘤伴Kasabach-Merritt现象的外科处理
Author: Dakan LIU ; Yuchun MA ; Xiaonan GUO ; Xiaoshuang ZHU ; Changxian DONG
Publication Type:Journal Article
From: Chinese Journal of Dermatology 2013;46(11):822-823
CountryChina
Language:Chinese
Abstract: Objective To analyze the surgical treatment of hemangioma of limbs complicated by Kasabach-Mcrritt phenomenon in children.Methods A retrospective study was carried out on 31 children with hemangioma of limbs complicated by Kasabach-Merritt phenomenon.Lower limbs were affected in 19 patients,and upper limbs in 12 patients.Twenty-six patients showed decreased platelet count ((2.6-60) × 109/L) and fibrinogen level (＜ 1 g/L),and 21 prolonged partial prothrombin time (＞ 50 seconds).All the patients who had responded poorly to medications including glucocorticoids received surgical treatment.Results Of these patients,30 were cured,and one died of massive blood loss.After surgical treatment,the platelet count returned to normal in 1-3 days in 25 patients,3-7 days in 4 patients,and more than 10 days in one patient.Conclusions For pediatric hemangiomas of limbs complicated by Kasabach-Merritt phenomenon,surgical treatment should be given as early as possible so as to reduce mortality in patients.