Inner Ear Anomalies Causing Congenital Sensorineural Hearing Loss: CT and MR Imaging Findings.
10.3348/jkrs.2005.52.3.165
- Author:
Hyun Sook HONG
1
;
Sang Hyun PAIK
;
Jang Gyu CHA
;
Seong Jin PARK
;
Joon Hee JOH
;
Jai Soung PARK
;
Dae Ho KIM
;
Hae Kyung LEE
;
Shi Chan KIM
Author Information
1. Department of Radiology, Soonchunhyang University Bucheon Hospital, Korea. hshong@schbc.ac.kr
- Publication Type:Case Report
- Keywords:
Ear abnormalities;
Computed tomography (CT);
Magnetic resonance imaging (MR)
- MeSH:
Brain;
Child;
Cochlear Implants;
Congenital Abnormalities;
Diagnosis, Differential;
Ear, Inner*;
Endolymphatic Sac;
Hearing Loss, Sensorineural*;
Humans;
Magnetic Resonance Imaging*;
Retrospective Studies;
Semicircular Canals;
Vestibular Aqueduct
- From:Journal of the Korean Radiological Society
2005;52(3):165-171
- CountryRepublic of Korea
- Language:English
-
Abstract:
Many congenital dysplasias of the osseous labyrinth have been identified, and the differential diagnosis of these dysplasias is essential for delivering proper patient management. We retrospectively reviewed the computed tomography (CT) and magnetic resonance (MR) imaging findings of 20 children who had congenital sensorineural hearing loss. The children included cases of enlarged vestibular aqueduct and endolymphatic sac (n=8), aplasia of the semicircular canal (n=4), lateral semicircular canal-vestibule dysplasia (n=3), common cavity malformations with a large vestibule (n=1), cochlear hypoplasia (n=1), Mondini's dysplasia with large vestibular aqueduct (n=1), Mondini's dysplasia with a large vestibule (n=1), and small internal auditory canal (n=1). Six cases were unilateral. Nine cases had combined deformities, and nine cases had cochlear implants. CT was performed with a 1.0-mm thickness in the direct coronal and axial sections with using bone algorithms. MR was performed with a temporal 3D T2 FSE 10-mm scan and with routine brain images. We describe here the imaging features for the anomalies of the inner ear in patients suffering from congenital sensorineural hearing loss.
