Advances of febrile infection-related epilepsy syndrome
10.3760/cma.j.issn.1673-4408.2013.02.016
- VernacularTitle:热性感染相关性癫(癎)综合征的研究进展
- Author:
Chengning ZHENG
;
Jingwei HU
- Publication Type:Journal Article
- Keywords:
Febrile infection;
Epilepsy syndrome;
Ketogenic diet
- From:
International Journal of Pediatrics
2013;(2):159-162
- CountryChina
- Language:Chinese
-
Abstract:
The scholars abroad have reported a group of previously normal children,who develop intractable focal epilepsy or status epilepticus after fever,followed by drug-resistant partial epilepsy and severe cognitive impairment,named febrile infection-related epilepsy syndrome (FIRES).There are unknown etiology,critical condition,poor prognosis and absent of specific changes on cerebrospinal fluid,biopsies and neuroimagings.No therapeutic agent is efficacious and ketogenic diet may be an alternative therapy in some reports.This study describes the clinical characteristics of FIRES.
