Progress in the diagnosis and treatment of hepatic Kasabach Merritt syndrome
10.3760/cma.j.issn.1007-8118.2012.06.028
- VernacularTitle:肝脏Kasabach-Merritt综合征的诊疗进展
- Author:
Han LIN
;
Yong MA
;
Lianxin LLU
- Publication Type:Journal Article
- Keywords:
Hepatic Kasabach-Merritt syndrotne;
Hemangioma;
Thrombocytopenia
- From:
Chinese Journal of Hepatobiliary Surgery
2012;18(6):486-488
- CountryChina
- Language:Chinese
-
Abstract:
Hepatic Kasabach-Merritt syndrome (KMS) is a highly complex and potentially fatal complication of severe hepatic hemangioma. Although hepatic KMS is rare,the death rate of victims is significant because it is often misdiagnosed upon presentation and thus receives improper treatment.Presently the literature lacks a systematic review of hepatic KMS.We have summarized its pathogenesis,diagnosis, systematic treatment, prognosis and outcomes in order to increase awareness of this deadly disease.
