Imaging feature of dysplasia epiphysealis hemimelica
10.3760/cma.j.issn.1005-1201.2012.06.013
- VernacularTitle:半肢骨骺发育异常的影像特征
- Author:
Zhenjiang ZHAO
;
Shiling LI
;
Jianling CUI
;
Yingcai SUN
- Publication Type:Journal Article
- Keywords:
Epiphyses;
Bone diseases developmental;
Diagnostic imaging
- From:
Chinese Journal of Radiology
2012;46(6):540-543
- CountryChina
- Language:Chinese
-
Abstract:
Objective To investigate the imaging features of dysplasia epiphysealis hemimelica (DEH).Methods Thirteen cases of DEH confirmed by pathology (between 1.5 to 19.0 years old)underwent X-ray scan.Additionally,CT scan was performed in one patient,MR scan was performed in one,and CT and MR scan were both performed in one.Results The lesions all occurred in lower limb.There were 32 lesions,and multiple lesions were detected in 8 cases.Lesions involved holo-epiphyses in 6 cases,Twenty-three lesions were in the medial limbs,3 were in the lateral limb.With Azouz classification,the limited form was identified in 5 cases,while the classic form was identified in 8 cases.Among 13 cases,there were 4 cases with ankle eversion,3 cases with the knock knee,2 cases with the ankle inversion,and 2 cases with the strephexopodia.The metaphysis of 8 cases were widened and deformed,and the provisional zone of calcification of 1case disappeared partly and the epiphysis closed prematurely.Conclusions One or multiple eccentric enlarged ossification center of unilateral or bilateral limb is the imaging feature of DEH.There is sporadic calcification or ossification on the prophase.The calcification or ossification can fuse each other to form agglomerate at the advanced stage.The bone can deform and shift when compressed by the mass,and bone defect can even occur.
