A Case of Typical Cogan's Syndrome with Aortitis.
10.4078/jkra.2010.17.3.301
- Author:
Hye Won KIM
1
;
Yun Jong LEE
;
Sung Hae CHANG
;
Han Hee RYU
;
Chan Young YUN
;
Eun Ha KANG
;
Eun Bong LEE
;
Yeong Wook SONG
Author Information
1. Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Cogan's syndrome;
Aortitis;
Arthritis
- MeSH:
Angiography;
Aorta, Thoracic;
Aortic Valve;
Aortic Valve Insufficiency;
Aortitis;
Arthritis;
Axis, Cervical Vertebra;
Cogan Syndrome;
Constriction, Pathologic;
Dyspnea;
Echocardiography;
Female;
Humans;
Iliac Artery;
Korea;
Mesenteric Artery, Superior;
Middle Aged;
Renal Artery;
Subclavian Artery;
Systemic Vasculitis;
Vasculitis
- From:The Journal of the Korean Rheumatism Association
2010;17(3):301-305
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Cogan's syndrome can accompany a variety of systemic vasculitides including aortitis. A 45-year-old woman with a history of typical Cogan's syndrome presented with orthopnea and exertional dyspnea. Echocardiography demonstrated severe aortic valve insufficiency. Computed tomographic angiography demonstrated active vasculitis affecting the ascending and descending aortas and also showed stenosis of the left subclavian artery, both renal arteries, the celiac axis, the superior mesenteric artery, and the right common iliac artery. She received high dose corticosteroid and then underwent an aortic valve replacement. This is the first case of Cogan's syndrome with aortitis in Korea.
