A Case of Churg-Strauss Syndrome with Endomyocardial Fibrosis.
10.4078/jkra.2010.17.3.306
- Author:
Hye Won KIM
1
;
Yeong Wook SONG
;
Sung Hae CHANG
;
Han Hee RYU
;
Ran SONG
;
Eun Bong LEE
;
Dae Won SON
;
You Young KIM
Author Information
1. Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea. ysong@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Churg-Strauss syndrome;
Endomyocardial fibrosis
- MeSH:
Cardiomyopathies;
Churg-Strauss Syndrome;
Dyspnea;
Endomyocardial Fibrosis;
Eosinophils;
Humans;
Magnetic Resonance Imaging;
Myocarditis;
Pericarditis
- From:The Journal of the Korean Rheumatism Association
2010;17(3):306-310
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Cardiac involvement is an important cause of mortality in patients with Churg-Strauss syndrome. The typical cardiac presentation of Churg-Strauss syndrome includes pericarditis, myocarditis, and cardiomyopathy. Endomyocardial fibrosis has rarely been described in patients with Churg-Strauss syndrome. We experienced a patient with Churg-Strauss syndrome who exhibited exertional dyspnea and endomyocardial fibrosis visualized as delayed enhancement on cardiac magnetic resonance imaging (MRI). After glucocorticoid treatment, the patient's symptom resolved, and the eosinophil count decreased to normal. Nine months later, the delayed-enhanced lesion on the cardiac MRI nearly disappeared. Here, we report a case of endomyocardial fibrosis in a patient with Churg-Strauss syndrome with a literature review.
