A Case of Hand-Schuller-Christian Disease with Exophthalmos.
- Author:
Yoon Soo JUN
1
;
Won Ryul LEE
;
Jae Ho KIM
Author Information
1. Department of Ophthalmology, Kangnam St, Mary's Hospital, Catholic Medical College, Seoul, Korea.
- Publication Type:Case Report
- MeSH:
Biopsy;
Drug Therapy;
Eosinophilic Granuloma;
Exophthalmos*;
Histiocytes;
Histiocytosis, Langerhans-Cell;
Humans;
Infant;
Male;
Ophthalmology
- From:Journal of the Korean Ophthalmological Society
1988;29(1):207-213
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Hand-Schuller-Christian disease, eosinophilic granuloma and Letterer-Siwe disease are classified as histiocytosis-x, on the basis of the underlying proliferation of histiocytes in all three conditions and of their indefinite etiology. The authors experienced a case of Hand-Schuller-Christian disease with exophthalmos. A 17 months old boy was admitted to our Dept. of Ophthalmology because of left exophthalmos since 2 months ago. A biopsy demonstrated that the lesion was Hand-Schuller-Christian disease. The patient was treated with chemotherapy and low dose radiation therapy. We report our experience with this patient along with the review of other papers in this report.
