A Case of Unilateral Retinitis Pigmentosa.
- Author:
Ke Hahn KIM
1
;
Young Hoon PARK
;
Duk Kee HAHN
Author Information
1. Department of Ophthalmology, College of Medicine, Yeungnam University, Taegu, Korea.
- Publication Type:Case Report
- Keywords:
Abnormal ERG;
Night blindness;
Unilateral retinitis pigmentosa
- MeSH:
Adult;
Female;
Humans;
Night Blindness;
Rare Diseases;
Retinitis Pigmentosa*;
Retinitis*;
Visual Fields
- From:Journal of the Korean Ophthalmological Society
1996;37(6):1090-1094
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Retinitis pigmentosa has been recognized as a symmetrical, bilateral, hereditary, tapetoretinal degeneration with night blindness, visual field loss, and abnormal ERG. Unilateral retinitis pigmentosa is a rather rare disease. Pedraglia described first reported a case of suspected unilateral retinitis pigmentosa in 1865. Francois and Verriest proposed the following four criteria of the unilateral retinitis pigmentosa: the presence of functional changes ophthalmoscopically typical primary pigmentary degeneration in the affected eye, the absence of a tapetoretinal dystrophy in the fellow eye with normal ERG over five years and exclusion of the inflammatory cause in the affected eye. We report a case of unilateral retinitis pigmentosa in 29 year-old female who has been followed for over five years.
