Clinical and radiologic study in intracranial epithelioid haemangioendothelioma and a literature review
- VernacularTitle:颅内血管内皮瘤临床及影像学分析并文献复习
- Author:
Jun ZHANG
;
Zonghui LIANG
;
Daoying GENG
;
Li ZHU
;
Ke LI
- Publication Type:Journal Article
- Keywords:
haemangioendothelioma;
computed tomography;
magnetic resonance imaging
- From:
China Oncology
2009;19(7):532-535
- CountryChina
- Language:Chinese
-
Abstract:
Background and purpose: Primary intracranial epithelioid haemangioendothelioma (EH) was rare. This study was to discuss the clinical pathological features, radiographic findings, treatment and prognosis of primary intracranial EH combined with literature review. Methods: We reviewed a case of EH reported from our hospital, and comprehensively analyzed the related literature. Results: Based on our report and review of the literature, EH is rare and with borderline or uncertain behavior. The original tumors demonstrated specific image features. The tumor usually appeared as a small nest or cords composed of eosinophilic epithlioid or spindled cells.Immunohistochemical assay were positive for endothelial markers CD31, CD34 and FⅧ. EH may be treated with complete surgical resection whenever possible and is sensitive to radiation. The EH has a favorable prognosis. Conclusion: EH has variable malignant potential, and should be differentiated from meningioma. Total resection and close follow-up is recommended. Additional radiotherapy is advised for residual tumors.