Analysis of onset age and cutaneous lesions in 54 patients with tuberous sclerosis
- VernacularTitle:54例结节性硬化症皮损的特点及其发生年龄分析
- Author:
Li ZHAO
;
Jing YE
;
Cunjiang LI
;
Yanni SUN
;
Changshun TONG
- Publication Type:Journal Article
- Keywords:
Tuberous sclerosis;
Skin manifestation;
Age of onset
- From:
Chinese Journal of Dermatology
2008;41(6):361-363
- CountryChina
- Language:Chinese
-
Abstract:
Objective To analyze the features of cutaneous lesions and age of onset of tuberous sclerosis(TS).Methods A total of 54 TS patients were recruited;their clinical data were analysed.Results The occurance of facial angiofibromas,periungual fibromas,hypomelanotic macules and shark macules was 72.5%,26%,70%and 48%,respectively,and the median age of onset of these lesions was 7,14,0.2 and 6 years,respectively,with a peak at 1-9,10-19,<1 and 1-9 years,respectively.Conclusions Cutaneous lesions are commonly seen in TS,and most of them develop early in life.