The diagnosis and therapy of intestinal lymphangiectasia,report of 15 cases
- VernacularTitle:小肠淋巴管扩张症15例的诊断和治疗
- Author:
Wande GENG
;
Wenbin SHEN
;
Yuguang SUN
;
Song XIA
;
Kun CHANG
- Publication Type:Journal Article
- Keywords:
Lymphangiectasia,intestinal;
Fatty acids;
Thoracic duct-vein anastomasis;
Bowel resection
- From:
Chinese Journal of General Surgery
2008;23(5):332-335
- CountryChina
- Language:Chinese
-
Abstract:
Objective To evaluate the diagnosis and therapy of intestinal lymphangiectasia.Methods In this study 15 patients were admitted in our hospital during recent 7 years.Clinical manifestations included hypoalbuminemia,symmetrical edema,emaciation,diarrhea and lymphopenia.Lymphangiography,lympanscintigraphy and biopsy were performed for diagnosis.Therapy conducted included conservative therapy,low-fat and medium-chain triglycerides(MCT)diet,albumin infusions,diuretics,total parenteral nutrition and octreotide.Surgical therapy ineluded thoracic duct-vein anastomasis and segmental resection.Results In this group 8 patients receiving conservative therapy were followed-up from 1.5 to 7 years(average 2.5 years).Symptoms were alleviated in 6 patients.Seven patients underwent operative therapy,among them,4 patients received thoracic duct-exterior jugular vein anastomasis and followed-up from 1 to 5 years,with symptoms mitigated in 2 patients.3 patients underwent local intestinal resection,follow-up from 1 to 3 years found one patient was cured,one was improved,and 1 patient died 3 months afterthe operation. Conclusion Intestinal lymphangiectasia is rather rare and there was no definite and effective therapy.
