Echocardiographic diagnosis of Berry syndrome
- VernacularTitle:Berry综合征的超声诊断
- Author:
Yali YANG
;
Xinfang WANG
;
Mingxing XIE
;
Qing LU
;
Lin HE
;
Xiaofang LU
;
Jing WANG
;
Ling LI
- Publication Type:Journal Article
- Keywords:
Echocardiography;
Heart defects,congenital;
Berry syndrome
- From:
Chinese Journal of Ultrasonography
2008;17(11):926-929
- CountryChina
- Language:Chinese
-
Abstract:
Objective To explore the value of transthoracic echocardiography in diagnosis of Berry syndrome and analyze the sonographic typing.Methods The echocardiographic results of 6 Berry patients were reviewed retrospectively.Their sonographic typing were also analyzed connected with the reports in the literature.Results The ultrasound diagnosis of 5cases were confirmed by surgery(3)or angiography(3) and the remain one infant was died 14 days after the echocardiographic procedure.The malformations of Berry syndrome consisted of the distal aorto-pulmonary septal defect(APSD),aortic origin of the right pulmonary artery(RPA),interruption of the aortic arch(5 cases,type A with patent ductus arteriosus)or coarctation of the aortic isthmus(1 case)with intact ventricular septum.In 6 cases,there were 2 sonographic types:(1)Type A(3 cases),the aorto-pulmonary septum was almost absent and the left and right pulmonary arteries remained widely separated,the blood of the RPA came almost from the aorta,the aortic arch was interrupted.(2)Type B(3 cases),the left and right pulmonary arteries remained adjacent and the bifurcation straddled the distal APSD,the blood of the RPA came from the aorta and the pulmonary trunk separately,the aortic arch was coarctated or interrupted. Conclusions The transthoracic echocardiography can be used to evaluate all containing malformations of Berry syndrome and it may be the first diagnostic choice.
