Radical Resection of Inferior Vena Cava Leiomyosarcoma; Hepatic and IVC Resection with Vascular Reconstruction and Kidney Autotransplantation.
- Author:
Jae Won JOH
1
;
Sung Joo KIM
;
In Seok CHOI
;
Jin Seok HEO
;
Se Woong LIM
;
Yong Il KIM
;
Byung Boong LEE
Author Information
1. Department of Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine, Korea.
- Publication Type:Case Report
- Keywords:
IVC leiomyosarcoma;
Radical resection
- MeSH:
Adrenal Glands;
Autografts*;
Blood Vessels;
Female;
Humans;
Kidney*;
Leiomyosarcoma*;
Liver;
Magnetic Resonance Imaging;
Middle Aged;
Recurrence;
Renal Veins;
Sarcoma;
Transplants;
Vena Cava, Inferior*
- From:The Journal of the Korean Society for Transplantation
1999;13(2):323-328
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Malignant sarcomas arising from the wall of blood vessels are extremely rare. It tends to enlarge by intra- or extra-luminal extension rather than infiltration, in some instances the tumor origin from the IVC invaded adjacent vital structures limit the extent of the resection. However, a wide and complete surgical resection provided the best chance for prolonged survival in patients. We experienced one case of IVC tumor invaded to right renal vein and liver. In a 52-year-old women suffering right frank pain, right upper retroperitoneal mass was found. In preoperative CT, MRI, Vena Cavogram, the mass was invaded to the right and quadate lobe of the liver, adrenal gland, and right renal vein. We performed the en-block resection including the right hepatic and quadate lobe, IVC and both kidney, and then IVC was reconstructed with graft (PTFE) and uninvolved left kidney was autotransplanted at right peritoneal space. Postoperatively, the patient was recovered satisfactory without complication. Because only way of preventing the development of recurrence is the radical resection of the IVC tumor including adjacent organs, a preoperative accurate staging and aggressive treatment are recommended.
