Primary leiomyosarcoma of the inferior vena cava
10.3760/cma.j.issn.1007-631X.2010.03.001
- VernacularTitle:原发性下腔静脉平滑肌肉瘤的诊治体会
- Author:
Jingjun JIANG
;
Xiaoming ZHANG
;
Xuemin ZHANG
;
Chenyang SHEN
;
Wei LI
;
Tao ZHANG
- Publication Type:Journal Article
- Keywords:
Leiomyosarcoma;
Surgical procedures,operative;
Vena cava,inferior
- From:
Chinese Journal of General Surgery
2010;25(3):177-179
- CountryChina
- Language:Chinese
-
Abstract:
Objective To investigate the clinical features,diagnosis and treatment of primary leiomyosarcoma of the inferior vena cflva(IVC).Methods We retrospectively analyzed the clinical data of 7 IVC leiomyosarcoma cases between June 2006 and April 2009,including clinical presentations,surgical procedures.pathological diagnosis and prognosis. Results Tumors were resected completely in 3 cases,among them.prosthetic grafts were used for IVC reconstruction in 2 eases.One patient underwent partialresection to recover the blood flow of the hepatic vein.Three cases underwent laparotomy and biopsy only.The diagnosis of IVC leiomyosarcoma was confirmed by pathology in all of 7 cases.Estrogen receptors and progesterone receptors were positive in 3 patients and negative in 4 patients.There was no perioperative mortality.Three cages who received tumor radical resection have been on warfarin for 6 months after operation and are doing well during a follow up for 8,32,and 33 months respectively with no tumor recunence and nor thrombosis formation.The cage undergoing tumor partial resection died of organdisfunction in 2 months.The three cases undergoing laparotomy only died of organ disfunction in 7 months.Conclusions The only effective way of treating primary leiomyosarcoma of the inferior vena cava is total resection with necessary reconstruction of the IVC.
