Isolated Right Ventricular Hypoplasia: A case report.
- Author:
Seog Ki LEE
1
;
Hong Joo SEO
;
Woong Han KIM
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Chosun University College of Medicine, Gwangju, Korea.
- Publication Type:Case Report
- Keywords:
Hypoplastic right ventricle;
Atrium;
Congenital heart defect
- MeSH:
Child;
Follow-Up Studies;
Heart Defects, Congenital;
Heart Ventricles;
Humans;
Male;
Myocardium;
Tricuspid Valve
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2003;36(9):683-686
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Isolated right ventricular hypoplasia is a rare clinical entity. We describe a case of right ventricular hypoplasia, single atrium and spongy myocardium of left ventricle. The volume of right ventricle was half the volume of left ventricle and z-value of tricuspid valve was -4 preoperatively. The patient, 6-year-old boy, underwent atrial partitioning with 3 mm fenestration. Postoperative course was smooth and he tolerated the biventricular state well during follow-up. Follow-up catherterization was done 27 months later. The tricuspid valve grew well (z-value=-0.4) and atrial septal fenestration is closed spontaneously. This article reports a case of successful biventricular repair in a patient with isolated right ventricular hypoplasia.
