Clinical Features and Surgical Outcomes of Sturge-Weber Syndrome with Glaucoma.
10.3341/jkos.2013.54.11.1737
- Author:
Jae Hwi PARK
1
;
Su Ho LIM
;
Soon Cheol CHA
Author Information
1. Department of Ophthalmology, Yeungnam University College of Medicine, Daegu, Korea. sccha@yumail.ac.kr
- Publication Type:Original Article
- Keywords:
Glaucoma;
Neurocutaneous findings;
Sturge-Weber syndrome;
Trabeculectomy
- MeSH:
Choroid;
Follow-Up Studies;
General Surgery;
Glaucoma*;
Hemangioma;
Humans;
Medical Records;
Retinal Detachment;
Retrospective Studies;
Seizures;
Sturge-Weber Syndrome*;
Trabeculectomy
- From:Journal of the Korean Ophthalmological Society
2013;54(11):1737-1747
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
PURPOSE: To report clinical manifestations including neurocutaneous and ocular findings and to evaluate outcomes of trabeculectomy in patients with Sturge-Weber syndrome. METHODS: The medical records of 10 eyes of 8 glaucoma patients with Sturge-Weber syndrome who were followed up for at least 1 year after trabeculectomy were reviewed retrospectively. We analyzed neurocutaneous and ocular findings, cumulative surgical success rates, and complications in patients with Sturge-Weber syndrome. RESULTS: The mean patient age at the time of surgery was 12.6 +/- 13.0 years and mean follow-up period was 71.6 +/- 81.8 months. All patients showed various clinical findings including facial hemangioma (8 patients), seizure (6 patients), intracranial lesion (6 patients), developmental delay (4 patients), conjunctival/episcleral hemangioma (4 eyes), and choroidal hemangioma (4 eyes). Postoperative success was achieved in 8 out of 10 eyes (80.0%). Postoperatively, serous retinal detachment occurred in 2 out of 4 eyes with preoperative diffuse choroidal hemangioma. CONCLUSIONS: Management of glaucoma associated with Sturge-Weber syndrome requires multidisciplinary treatment because of systemic involvement. Trabeculectomy appears to be an effective and relatively safe surgical option for glaucoma associated with Sturge-Weber syndrome. However, serious complications such as serous retinal detachment should be considered when planning trabeculectomy for patients with diffuse choroidal hemangioma.
