A Case of Frozen Elephant Trunk Technique for Aortic Dissection in Loeys-Dietz Syndrome
10.4326/jjcvs.44.330
- VernacularTitle:Loeys-Dietz 症候群に合併した大動脈解離に対するオープンステントグラフト手術の1例
- Author:
Tomokuni Furukawa
;
Naomichi Uchida
;
Yoshitaka Yamane
;
Shingo Mochizuki
;
Kazunori Yamada
;
Takaaki Mochizuki
- Publication Type:Journal Article
- Keywords:
open stent graft;
frozen elephant trunk technique;
Loeys-Dietz syndrome;
aortic dissection;
aortic aneurysm
- From:Japanese Journal of Cardiovascular Surgery
2015;44(6):330-333
- CountryJapan
- Language:Japanese
-
Abstract:
The patient was a 37 year-old man. We diagnosed Loeys-Dietz syndrome based on his physical characteristics that were widely spaced eyes and brachycephaly etc. Since he developed De Bakey III b aortic dissection 3 months later, he needed surgical repair for saccular-shaped distal arch aortic aneurysm. We performed total aortic arch replacement for the aneurysm and valve-sparing aortic root reconstruction for dilatation of the Valsalva sinus. Furthermore we performed the frozen elephant trunk technique for residual aortic dissection at the same time. After 18 months from the operation, we were able to recognize by computed tomography that the false lumen of the aorta next to the stent graft was thrombosed and absorbed and finally disappeared. The stent graft treatment for patients with connective tissue disease might be an effective method and deserves more attention.
