A Case Report of Aortic Valve Replacement for a Patient with von Willebrand Disease
10.4326/jjcvs.44.292
- VernacularTitle:Von Willebrand 病患者に対する大動脈弁置換術の1例
- Author:
Kazue Nakashima
;
Yukihiro Yoshimura
;
Shuji Toyama
;
Yoshiyuki Maekawa
;
Tadanori Minagawa
;
Mitsuaki Sadahiro
- Publication Type:Journal Article
- Keywords:
Von Willebrand's disease;
aortic valve replacement;
vWF infusion
- From:Japanese Journal of Cardiovascular Surgery
2015;44(5):292-295
- CountryJapan
- Language:Japanese
-
Abstract:
We report a 30-year-old patient with von Willebrand disease who received AVR under cardio-pulmonary bypass. AR was diagnosed at the age of 13, and von Willebrand disease was revealed after cardiac catheterization because of a bleeding episode. His von Willebrand factor (vWF) activity was significantly low, 43% of normal. Infusion of vWF concentrates (Confact F®) was administered before surgery. AVR was safely performed and no bleeding complications occurred during the perioperative period. Blood transfusion was unnecessary, vWF infusion was considered to be very useful.
