A Rare Case of Extracardiac Growing Angiomyolipoma Originating from the Interatrial Septum
10.4326/jjcvs.44.237
- VernacularTitle:心臓外に発育した心房中隔原発血管筋脂肪腫の1例
- Author:
Junji Yanagisawa
;
Atsuo Maekawa
;
Sadanari Sawaki
;
Satoshi Hosino
;
Yasunari Hayashi
;
Masayoshi Tokoro
;
Toshiaki Ito
- Publication Type:Journal Article
- Keywords:
cardiac tumor;
angiomyolipoma;
HMB45
- From:Japanese Journal of Cardiovascular Surgery
2015;44(4):237-240
- CountryJapan
- Language:Japanese
-
Abstract:
A 58-year-old man was admitted with a complaint of exertional chest discomfort. A mass, 53×55×66 mm in size, was detected in the transverse sinus of the pericardium, just cranial to the inter-atrial septum with enhanced chest CT. We performed resection of the tumor under cardiopulmonary bypass. Histopathological findings showed that the tumor was angiomyolipoma originated from the heart. Angiomyolipoma is a benign tumor, most frequently found in the kidney or liver and usually associated with tuberous sclerosis. Extra-cardiac growth of the cardiac angiomyolipoma is extremely rare, and only few have been reported previously.
