A Case of Congenital Hypoprothrombinemia.
- Author:
Jong Kwang LEE
;
Hae Won CHEON
;
Jung Hwa LEE
;
Kwang Chul LEE
;
Soon Kyum KIM
- Publication Type:Case Report
- MeSH:
Brain;
Female;
Fibrinogen;
Hemorrhage;
Humans;
Hypoprothrombinemias*;
Lateral Ventricles;
Male;
Menorrhagia;
Prothrombin;
Prothrombin Time;
Skin;
Thrombin Time;
Tomography, X-Ray Computed;
Tooth Extraction;
Vomiting
- From:Journal of the Korean Pediatric Society
1994;37(3):422-428
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Congenital hypoprothrombinemia is a rare congenital coagulation defect. The clinical signs are manifestation of generalized tendency such as; mucosal bleeding, hypermenorrhea and post tooth extraction hemorrage. It is associated with prolongation of PT and PTT with normal thrombin time and decreased serum prothrombin level. A case with congenital hypoprothrombinemia was experienced by the authors. A 36 days old male baby was admitted with palor skin and vomiting started one day before admission. Right side brain parenchymal hemorrhage and left shift of lateral ventricle were on brain CT scan. Prologation of prothrombin time and partial prothrombin time with decreased serum prothrombin level were resulted. Serum factor I, V, VII, VIII, IX and X were within normal level. We report a case congenital hypoprothrombinemia with a brief review of relaed literatures.
