Valvuloplasty of Persistent Truncus Arteriosus with Pentacuspid Truncal Valve Insufficiency
10.4326/jjcvs.42.183
- VernacularTitle:5弁尖を有する総動脈幹遺残の弁形成術の経験
- Author:
Takayuki Abe
;
Koji Nomura
;
Katsushi Kinouchi
;
Ko Yoshihiro
- Publication Type:Journal Article
- Keywords:
persistent truncus arteriosus;
truncal valve;
pentacuspid;
valvuloplasty
- From:Japanese Journal of Cardiovascular Surgery
2013;42(3):183-185
- CountryJapan
- Language:Japanese
-
Abstract:
A neonate, presenting with cyanosis, received the diagnosis of persistent truncus arteriosus with truncal valve stenosis with insufficiency. Her disease was classified as persistent truncus arteriosus Van Praagh type A1, or Collett and Edwards type I. At the age of 2 months, she underwent a modified Blalock-Taussig shunt, and her operative team was waiting for adequate body weight gain before performing further surgery. At the age of 1 year, however, she began to have repeated episodes of congestive heart failure due to severe tricuspid valve regurgitation and truncal valve insufficiency. When she reached 18 months of age, she underwent a definitive operation including a truncal valve plasty, VSD patch closure, and a right ventricular outflow tract reconstruction. Postoperative echocardiography 6 months after surgery showed a good truncal valve function with minimal regurgitaion. Truncal valve surgery is a challenging operation ; we report a successfully treated case, though the patient will require extensive follow-up.