A Case of Self-Healing Reticulohistiocytosis.
- Author:
Eun Jung SHIM
1
;
Eun Hye PARK
;
Hyun Sang CHO
;
Jae Kook CHA
;
Eun Sook NAM
;
Hae Ran LEE
Author Information
1. Department of Pediatrics and 1Pathology, College of Medicine, Hallym University, Seoul, Korea. hscho@www.hallym.or.kr
- Publication Type:Case Report
- Keywords:
Self-healing reticulohistiocytosis
- MeSH:
Bone Marrow;
Histiocytes;
Humans;
Hypertriglyceridemia;
Infant;
Lymphocytosis;
Pancytopenia;
Skin
- From:Korean Journal of Pediatric Hematology-Oncology
2001;8(1):132-136
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Self-healing reticulohistiocytosis is a perinatal disease characterized by rapidly developing and involuting benign histiocytic infiltration of the skin and other organ. We had recently experienced a case of a self-healing reticulohistiocytosis in 99-day-old infant who presented with multiple erythematous nodular lesions on face and trunk and pancytopenia. Our case differed from those previously reported in that extracutaneous involvement was found. The patient had pancytopenia, hypertriglyceridemia, hypofibrinogenemia hyperferritinemia and hepatosplenomegaly as well as skin lesions. Bone marrow showed a marked lymphocytosis with many histiocytes. We described a detailed clinical features of this case and reviewed the literatures.
