A Case of Marfan's Syndrome with Acute Aortic Dissection during Pregnancy
10.4326/jjcvs.34.116
- VernacularTitle:妊娠後期に急性大動脈解離を発症したＭａｒｆａｎ症候群の１例
- Author:
Takahiro Inoue
;
Yoshimasa Sakamoto
;
Hiroshi Okuyama
;
Makoto Hanai
;
Noriyasu Kawada
;
Gen Shinohara
;
Kazuhiro Hashimoto
- Publication Type:Journal Article
- From:Japanese Journal of Cardiovascular Surgery
2005;34(2):116-119
- CountryJapan
- Language:Japanese
-
Abstract:
We present a case of Marfan's syndrome with acute aortic dissection during the trimester of her pregnancy, who underwent a Bentall operation 2 days after emergency cesarean section. A 24-year-old woman during the 31st week of pregnancy visited our emergency room due to sudden onset of chest and back pain, though she had no abnormality until this event. Because of her tall height, spider fingers, positive wrist sign, visual disorder and scoliosis, she was given a diagnosis of Marfan's syndrome. Enhanced CT and cardiac ultrasonography revealed that she was suffering from acute aortic dissection with annulo-aortic ectasia. Since it was difficult for her to continue with her pregnancy, she underwent emergency cesarean section and gave birth to a male baby weighted 1, 706g. Although there was little likelifood of early thrombus formation in the false lumen or significant aortic regurgitation indicating an emergency operation, fear of massive bleeding from her uterus and the exfoliated surface of the placenta after cesarean section required an observation period of 2 days. We performed a Bentall operation successfully after careful sedation, ventilation and blood pressure control for 2 days.
