A Case Report of Aortic Root Replacement, Mitral Valve Replacement and Extended Thoracic Aorta Replacement for a Patient with Marfan's Syndrome
10.4326/jjcvs.33.282
- VernacularTitle:Ｍａｒｆａｎ症候群に対する大動脈基部置換，僧帽弁置換，上行弓部下行大動脈置換同時手術の１治験例
- Author:
Iwao Taniguchi
;
Keisuke Morimoto
;
Akira Marumoto
;
Yousin Adachi
- Publication Type:Journal Article
- From:Japanese Journal of Cardiovascular Surgery
2004;33(4):282-286
- CountryJapan
- Language:Japanese
-
Abstract:
A 39-year-old woman with Marfan's syndrome was referred with a symptom of exertional dyspnea, had mitral valve regurgitation, annuloaortic ectasia with aortic valve regurgitation and Stanford B type chronic aortic dissection. She was successfully treated with a one-stage operation, consisting of aortic root replacement with the Carrel patch method, mitral valve replacement and extended replacement of the thoracic aorta (ascending, arch and thoracic descending aorta), through median sternotomy and left antero-axillary thoracotomy. This operation was performed under hypothermic circulatory arrest with continuous retrograde cerebral perfusion. The postoperative course was uneventful. Although the operation may include complicated procedures, it is important to perform a sufficient operation corresponding to the patient's condition and lesions, employing the most advanced surgical techniques, such as circulatory arrest, myocardial protection and so on.
