One-Staged Operation for Stanford Type A Aortic Dissection, AAE, Mitral Valve Regurgitation and Pectus Excavatum in a Patient with Marfan's Syndrome.
10.4326/jjcvs.31.278
- VernacularTitle:上行大動脈解離，ＡＡＥ，僧帽弁閉鎖不全，漏斗胸に対して一期的根治術を施行したＭａｒｆａｎ症候群の１例
- Author:
Chiho Tokunaga
;
Tomoaki Jikuya
;
Wahei Mihara
;
Jun Seita
;
Kazuhiro Naito
;
Yasushi Terada
;
Toshio Mitsui
- Publication Type:Journal Article
- Keywords:
AAE (annuloaortic ectasia)
- From:Japanese Journal of Cardiovascular Surgery
2002;31(4):278-281
- CountryJapan
- Language:Japanese
-
Abstract:
A 22-year-old man was hospitalized due to severe back pain having being diagnosed as Stanford type A aortic dissection, AAE, mitral regurgitation and pectus excavatum associated with Marfan's syndrome. A single staged operation including ascending aortic replacement, mitral valve replacement and sternal turnover with a rectus muscle pedicle was carried out in order to keep the blood supply to the plastron to reduce the risk of infection during such a long operation. By this approach, it was found that the operative field was excellent and postoperative hemodynamics were stable. However, frail plastron occurred because of difficulties in keeping the patient stabilized because of severe pain thus re-fixation was required. The necessity of strong pain control after such an operation was also recognized.
