Three Cases of Chronic Type A Aortic Dissection with Connective Tissue Disease.
10.4326/jjcvs.30.51
- VernacularTitle:結合組織代謝異常症を伴う慢性Ａ型解離性大動脈りゅう３治験例
- Author:
Yoshihiro Ko
;
Tadashi Okubo
;
Ryouhei Hoshino
;
Yoshiyuki Kamigaki
- Publication Type:Journal Article
- From:Japanese Journal of Cardiovascular Surgery
2001;30(1):51-54
- CountryJapan
- Language:Japanese
-
Abstract:
We performed a modified Bentall operation and aortic arch replacement simultaneously in three cases of chronic type A aortic dissection with connective tissue disease. Two of the subjects were men. Ages ranged from 37 to 48 years. There were two cases of Marfan's syndrome, and one case of cystic medial necrosis. All patients had annuloaortic ectasia (AAE), severe aortic regurgitation (AR) and marked dilatation at the base and arch of the aorta with extensive dissecting lesions. Widespread, progressive vascular lesions are often seen, especially among cases of dissecting aneurysm of the aorta with connective tissue disease, and there is a high probability that new vascular lesions and valvular diseases will result after surgery. Therefore, cases must be followed, keeping in mind the possibility of early extended aortic operation and secondary surgery.
