Operation for Acute Aortic Dissection 13 Years after Operation for Funnel Chest in Marfan Syndrome.
10.4326/jjcvs.30.33
- VernacularTitle:胸骨翻転術後１３年目に急性Ａ型解離を発症したＭａｒｆａｎ症候群に対する緊急手術
- Author:
Yuji Kanaoka
;
Kazuo Tanemoto
;
Takashi Murakami
;
Keiichiro Kuroki
;
Hitoshi Minami
;
Masahiko Kuinose
- Publication Type:Journal Article
- Keywords:
flail chest
- From:Japanese Journal of Cardiovascular Surgery
2001;30(1):33-35
- CountryJapan
- Language:Japanese
-
Abstract:
Abnormalities of the skeleton and joint as well as ophthalmic symptoms and cardiovascular abnormalities are found in Marfan's syndrome, one of the connective tissue diseases associated with autosomal dominant inheritance. A 34-year-old man was operated on for Stanford type A acute aortic dissection that developed 13 years after sternal turnover surgery for funnel chest. After approaching by median incision made on the sternum, composite graft replacement and aortic arch replacement were performed. After surgery, the sternum at the site of reflections became unsteady, causing flail chest, which required internal fixation with an artificial respirator for 15 days. A patient with Marfan's syndrome may undergo cardiovascular operation twice or more throughout his lifetime. Where a longitudinal incision is made on the sternum after operation on the funnel chest, care should be exercised even if it is a long time after surgery. In this sense, minimal invasive surgery with a steel bar inserted percutaneously, a surgical technique that has come to be used recently, should be useful.
