Successful Surgical Repair of Double-Outlet Right Ventricle in a Patient with Congenital Mitral Valve Stenosis.
10.4326/jjcvs.25.321
- VernacularTitle:僧帽弁狭窄を合併した両大血管右室起始症の１手術
- Author:
Yoshito Inoue
;
Toyoki Fukuda
;
Takaaki Suzuki
;
Akira Aki
- Publication Type:Journal Article
- From:Japanese Journal of Cardiovascular Surgery
1996;25(5):321-324
- CountryJapan
- Language:Japanese
-
Abstract:
A 2-year-old boy was admitted to our service with a diagnosis of double-outlet right ventricle (DORV) complicated by mitral valve stenosis. On echocardiographic measurement, the mitral annulus was 11mm (69% of normal) in diameter and 1.67cm2/m2 in annular area. He underwent intraventricular tunnel repair and patch reconstruction of the right ventricular outflow tract under cardiopulmonary bypass. No attempt was made to operate on the mitral valve. DORV with mitral stenosis is a rare cardiac anomaly, the last 20 years only 21 cases have been reported, of which only 4 were cases with hypoplastic mitral rings. Although the patient made an uneventful recovery and remains well 5 months after surgery, a close observation is required for the mitral valve stenosis.
