Arteriosclerosis Obliterans with Huge Multiple Leg Ulcers in a Patient with X-linked Ichthyosis.
10.4326/jjcvs.23.68
- VernacularTitle:伴性遺伝性魚鱗せんに発症した多発性巨大下腿潰ようを伴った閉塞性動脈硬化症の一例
- Author:
Tohru Sakurada
;
Makoto Kamada
;
Yoshiki Shibata
;
Itsuro Yamagishi
;
Tadaaki Abe
- Publication Type:Journal Article
- From:Japanese Journal of Cardiovascular Surgery
1994;23(1):68-71
- CountryJapan
- Language:Japanese
-
Abstract:
A 64-year-old man with arteriosclerosis obliterans with huge multiple ulcers of the left leg was admitted for surgery. He had ichthyosis, and was diagnosed as X-linked ichthyosis by reduced steroid sulfatase activity and clinical examinations. Angiography revealed occlusions of the left common and external iliac arteries, left femoral artery, and right femoral artery. Aorto-left femoral bypass with a gelatin impregnated Dacron prosthesis and left femoro-popliteal bypass with a reversed saphenous vein graft were performed. Postoperatively the leg ulcers gradually healed and the patient was discharged in good condition. Leg ulcers with arteriosclerosis obliterans in patient with X-linked ichthyosis should be treated by the arterial reconstruction in the same way as in case with normal skin.