A Case of Primary Cardiac Angiosarcoma.
10.4326/jjcvs.22.493
- VernacularTitle:原発性心臓血管肉腫の１例
- Author:
Kenji TAKAHASHI
;
Atushi NARITA
;
Koji NAGAO
;
Satoshi IWABUCHI
;
Sohei SUZUKI
;
Hisaaki KOIE
- Publication Type:Journal Article
- From:Japanese Journal of Cardiovascular Surgery
1993;22(6):493-496
- CountryJapan
- Language:Japanese
-
Abstract:
Cardiac angiosarcoma is a rare disease which occurs most often in young males and has a remarkably unfavorable prognosis. We experienced one male case aged 46 who had an initial symptom of cardiac tamponade due to rupture of the right ventricle. Hemostasis was made under extracorporeal circulation, and the patient was discharged temporarily. However, a large volume of hemoptysis occurred from right B6 about 1 month after discharge, because of which resection of the right lower lobe was performed. Tumorous cells identical to those in the perforated cardiac region were detected in the resected tissue, and it was diagnosed histopathologically that the cardiac rupture was caused by angiosarcoma, resulting in pulmonary metastasis. Multiple pulmonary metastases were observed in bilateral lung following fields by CT, but administration of CDDP in iv×2 and in 150mg/day cyclophosphamide, the pulmonary metastases disappeared completely on CT on the 45th day. However, the metastases recurred soon thereafter without responding to chemotherapy, and the patient died 5 months after diagnosis of this disease because of exacerbated dyspnea.
