The Surgical Treatment of Endocardial Fibroelastosis and Endomyocardial Fibrosis.

VernacularTitle:乳児期に発症した心内膜線維弾性症と心内膜心筋線維症の手術治験例と長期予後
Author: Hitoshi YAMAUCHI ; Shigeo TANAKA ; Junichi NINOMIYA ; Kiyoshi KOIZUMI ; Masami OCHI ; Kouichi TERADA ; Shuji HARAGUCHI ; Jirou HONDA ; Tadahiko SUGIMOTO ; Tasuku SHOUJI
Publication Type:Journal Article
From:Japanese Journal of Cardiovascular Surgery 1992;21(6):614-618
CountryJapan
Language:Japanese
Abstract: We performed mitral valvuloplasty for 25 months old infant with endocardial fibroelastosis (EFE) and 21 months old infant with endomyocardial fibrosis (EMF). These two patients showing good post operative cause, have been followed up during 10 and 1 years respectively. The EFE and EMF are severe and progressive restrictive cardiomyopathy of unknown etiology. Most of cases with EFE and EMF have an enlarged left ventricle with incompetent atrioventricular valve. The prognosis of these patient is usually poor. We believe that the surgical treatment in early phase may be able to improve heart failure and also to protect the progression of these disease. This case with EMF is the first report of successfull surgical treatment for the patients with severe congestive heart failure whithin one year after birth in Japan.