A Surgical Case for Acute Heart Failure in a 1-month-old Infant with a Right Cervical Aortic Arch
10.4326/jjcvs.41.128
- VernacularTitle:頸部大動脈弓症の1カ月児に対する手術経験
- Author:
Koji Nomura
;
Takayuki Abe
;
Yoshihiro Ko
- Publication Type:Journal Article
- Keywords:
right cervical aortic arch;
22q11 deletion;
coarctation;
ventricular dysfunction;
infant
- From:Japanese Journal of Cardiovascular Surgery
2012;41(3):128-131
- CountryJapan
- Language:Japanese
-
Abstract:
A 2-day-old male baby was referred to our hospital because of a heart murmur. We diagnosed as a right cervical aortic arch, and coarctation between the right carotid and right subclavian artery. On echocardiography, the velocity at the coarctation was 1.8 m/s, the left ventricular ejection fraction (LVEF) was 53%, and he was asymptomatic during the neonatal period. A chromosome examination showed a deletion of 22q11 syndrome. At 1 month, he weighted 3.8 kg and was readmitted to our hospital for wheezing. Echocardiography showed a left ventricular dysfunction with LVEF of 24%. The coarctation velocity increased to 5.1 m/s. An urgent operation was performed because of a severely depressed cardiac function. His LVEF increased to 67%, and the velocity was less than 1 m/s postoperatively, and he was discharged on postoperative day 32. We report a rare neonatal surgical case of a right cervical arch with a coarctation.