Aortic Root Replacement for Perivalvular Leakage after Aortic Valve Replacement for Marfan Syndrome with Severe Thoracic Deformity
10.4326/jjcvs.40.14
- VernacularTitle:著明な胸郭変形を伴う Marfan 症候群における大動脈弁置換術後弁周囲逆流に対する基部置換術の1例
- Author:
Takako Nishino
;
Toshihiko Saga
;
Hitoshi Kitayama
;
Susumu Nakamoto
;
Kiyoaki Takaba
;
Kousuke Fujii
;
Shintaro Yukami
- Publication Type:Journal Article
- Keywords:
Marfan syndrome;
perivalvular leakage;
thoracic deformities;
secondary surgery
- From:Japanese Journal of Cardiovascular Surgery
2011;40(1):14-18
- CountryJapan
- Language:Japanese
-
Abstract:
The number of operations performed for cardiovascular disease has increased since recent improvements in diagnostic and the therapeutic technology have led to a remarkable increase in the life expectancy of patients with Marfan syndrome. On the other hand, operative procedures can be difficult when patients have complications of connective tissue abnormalities such as thoracic deformities, lung diseases and ophthalmic lesions. Although recent surgical outcomes have improved, those of secondary surgery are more difficult. We describe aortic root replacement to treat perivalvular leakage after aortic valve replacement in a patient with Marfan syndrome with a severe thoracic deformity.
