Steroid Therapy in a Surgical Treated Case of Ventricular Septal Defect with Congenital Adrenocortical Insufficiency
10.4326/jjcvs.38.276
- VernacularTitle:心室中隔欠損症に先天性副腎皮質機能不全を合併した乳児に対し周術期糖質コルチコイド補充療法を施行した1手術例
- Author:
Susumu Oozawa
;
Shingo Kasahara
;
Yasuhiro Kotani
;
Shunji Sano
- Publication Type:Journal Article
- From:Japanese Journal of Cardiovascular Surgery
2009;38(4):276-279
- CountryJapan
- Language:Japanese
-
Abstract:
A very rare case of congenital adrenocortical insufficiency accompanied with ventricular septal defect, is presented. Surgical treatment together with glucocorticoid replacement therapy was performed. The patient, a 4-month-old girl with congenital adrenocortical insufficiency, had been treated with a long-term adrenocortical hormones replacement. Surgical treatment for ventricular septal defect was applied in order to reduce the risk of heart failure. The administration dose of glucocorticoid was determined according to the body surface area and chronologic change of serum cortisol. Following the surgical treatment, and with adequate glucocorticoid replacement, the patient showed a good clinical outcome. In conclusion, we showed a beneficial treatment protocol with adequate glucocorticoid replacement in open heart surgery for a case of congenital adrenocortical insufficiency.
