Successful Surgical Treatment of Pentacuspid Aortic Valve with Severe Aortic Regurgitation
10.4326/jjcvs.37.53
- VernacularTitle:非常に希な先天性大動脈5尖弁による大動脈弁閉鎖不全症の1手術例
- Author:
Sokichi Kamata
;
Nobuo Sakagoshi
;
Toshihiro Ohata
;
Yoshikado Sasako
- Publication Type:Journal Article
- From:Japanese Journal of Cardiovascular Surgery
2008;37(1):53-55
- CountryJapan
- Language:Japanese
-
Abstract:
A 38-year-old woman was admitted due to an abnormal ECG and dyspnea on effort. Transoesophageal echocardiography and cardiac computed tomography (CT) showed severe aortic regurgitation (AR) due to pentacuspid aortic valve, which consisted of 4 relatively equal cusps and 1 larger cusp. Mild mitral regurgitation, atrial septal defect (ASD) and coronary-pulmonary artery fistula were complicated for her. She underwent aortic valve replacement, mitral valve annuloplasty, direct closures of ASD and coronary-pulmonary artery fistula. The pathophysiology of the resected aortic valve showed 4 equal size cusps and a large one with mild myxomatous change. Aortic valve regurgitation due to pentacuspid aortic valve is extremely rare and there was little report concerning it in the literature. We reported the surgical repair of this rare case of severe AR due to pentacusupid aortic valve.
