Parry-Romberg Syndrome with Intermittent Exotropia.
- Author:
Young Soo KIM
1
;
Seonhye KIM
;
Wook jin CHOI
;
Oh Young KWON
;
Soo Kyung KIM
;
Heeyoung KANG
;
Ki Jong PARK
;
Nack Cheon CHOI
;
Byeong Hoon LIM
Author Information
1. Department of Neurology, Gyeongsang National University School of Medicine, Gyeongsang National University Hospital, Jinju, Korea.
- Publication Type:Case Report
- Keywords:
Intermittent exotropia;
Parry-Romberg syndrome
- MeSH:
Atrophy;
Enophthalmos;
Exotropia;
Eye;
Facial Hemiatrophy;
Female;
Humans;
Skin;
Subcutaneous Tissue
- From:Journal of the Korean Neurological Association
2012;30(2):141-144
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Parry-Romberg syndrome, or progressive facial hemiatrophy, is a rare and acquired neurocutaneous disease of unknown etiology that is classically characterized by progressive and self=limited atrophy of the skin, subcutaneous tissues, and underlying bone structures. Ophthalmic involvement is reportedly not uncommon, and the most common ocular finding is enophthalmos. Here we report a 46=year=old woman with Parry=Romberg syndrome who presented with intermittent exotropia of the right eye. To the best of our knowledge, this is the first description of intermittent exotropia in a patient with Parry-Romberg syndrome.
