A Case of Chronic Progressive External Ophthalmoplegia.
- Author:
Won Kyu SHIN
1
;
Byung Su CHOI
;
Hanho SHIN
Author Information
1. Department of Ophthalmology, College of Medicine, Soonchunhyang University, Hospital, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
CPEO;
Abnormal mitochondria;
ptosis;
ragged red fiber
- MeSH:
Blepharoptosis;
Endocrine Glands;
Female;
Heart;
Humans;
Inclusion Bodies;
Microscopy, Electron;
Middle Aged;
Mitochondria;
Ophthalmoplegia, Chronic Progressive External*;
Paralysis;
Retina;
Skeleton
- From:Journal of the Korean Ophthalmological Society
1995;36(1):120-124
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Chronic progressive external ophthalmoplegia(CPEO) is rare syndrome, which is characterized by slowly progressive blepharoptosis, paralysis of extraocular muscle and has involvement of other organs, particularly the retina, heart, endocrine gland, and bony skeleton. Histological examination of muscle showes characteristic ragged red fibers. Electron microscopy reveals a number of abnormal mitochondria which contain paracrystalline inclusion bodies. We experienced a 50-year-old female with CPEO, that was pathologically proven by electron microscopy and bilateral levator levator advancements were given for ptosis.
