A cases of Congenital Nephrogenic Diabetes Insipidus with Bilateral Hydronprosis.
- Author:
Young Mo SOHN
1
;
Chul LEE
;
Pyung Kil KIM
;
Duk Jin YUN
Author Information
1. Department of Pediatrics, College of Medicize Yonsei University Seoul, Korea.
- Publication Type:Original Article
- MeSH:
Adolescent;
Diabetes Insipidus, Nephrogenic*;
Family Characteristics;
Humans;
Hydronephrosis;
Indomethacin;
Male;
Osmolar Concentration;
Pedigree;
Urinary Bladder, Neurogenic
- From:Journal of the Korean Pediatric Society
1980;23(5):417-422
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 13 year old boy was diagnosed as primary nephrotic diabetesinsipidus, whose symptom has been devloped from 3 years of age, subsequetly he developed bilateral hydronephrosis and neurogenic bladder. His pedigree could be explored 5 generations and represented inheritace as X-linked recesslive transmission, He was treated with indomethacin 2mg/Kg/day plus chlorothiazid 500mg/dau and this new method shows markedly decreased urine outpur and increased urine osmolarity.